[article]
| Titre : |
Aqueductal stenosis in X-linked hydrocephalus: a secondary phenomenon? |
| Type de document : |
texte imprimé |
| Auteurs : |
P. LANDRIEU, Auteur ; Gilles LYON, Auteur ; J. NINANE, Auteur ; G. FERRIERE, Auteur |
| Année de publication : |
1979 |
| Article en page(s) : |
p.637-642 |
| Langues : |
Anglais (eng) |
| Index. décimale : |
PER Périodiques |
| Résumé : |
Two cases of x-linked hydrocephalus are reported. One underwent postmortem examination: serial sections of the brain stem failed to show stenosis of the aqueduct, the mean and minimal cross-sectional areas of which were normal. However, there were some morphological changes which were compatible with a mechanical compression of the brain stem. It is postulated that in the Bickers and Adams syndrome of x-linked hereditary hydrocephalus the primary defect is a communicating hydrocephalus leading usually, but not always, to aqueductal stenosis. The importance of electrophysiological investigations for the correct diagnosis of the characteristic clasped-thumb deformity is also indicated. |
| Permalink : |
https://www.cra-rhone-alpes.org/cid/opac_css/index.php?lvl=notice_display&id=500 |
in Developmental Medicine & Child Neurology > 21-5 (October 1979) . - p.637-642
[article] Aqueductal stenosis in X-linked hydrocephalus: a secondary phenomenon? [texte imprimé] / P. LANDRIEU, Auteur ; Gilles LYON, Auteur ; J. NINANE, Auteur ; G. FERRIERE, Auteur . - 1979 . - p.637-642. Langues : Anglais ( eng) in Developmental Medicine & Child Neurology > 21-5 (October 1979) . - p.637-642
| Index. décimale : |
PER Périodiques |
| Résumé : |
Two cases of x-linked hydrocephalus are reported. One underwent postmortem examination: serial sections of the brain stem failed to show stenosis of the aqueduct, the mean and minimal cross-sectional areas of which were normal. However, there were some morphological changes which were compatible with a mechanical compression of the brain stem. It is postulated that in the Bickers and Adams syndrome of x-linked hereditary hydrocephalus the primary defect is a communicating hydrocephalus leading usually, but not always, to aqueductal stenosis. The importance of electrophysiological investigations for the correct diagnosis of the characteristic clasped-thumb deformity is also indicated. |
| Permalink : |
https://www.cra-rhone-alpes.org/cid/opac_css/index.php?lvl=notice_display&id=500 |
|  |
Aqueductal stenosis in X-linked hydrocephalus: a secondary phenomenon? in Developmental Medicine & Child Neurology, 21-5 (October 1979)