Behavior therapy for a child with Lesch-Nyhan syndrome / Marilyn BULL in Developmental Medicine & Child Neurology, 20-3 (June 1978)

Public ISBD [article]  inDevelopmental Medicine & Child Neurology > 20-3 (June 1978) . - p.368-375 Titre : Behavior therapy for a child with Lesch-Nyhan syndrome Type de document : Texte imprimé et/ou numérique Auteurs : Marilyn BULL, Auteur ; Francesca LAVECCHIO, Auteur Année de publication : 1978 Article en page(s) : p.368-375 Langues : Anglais (eng) Index. décimale : PER Périodiques Résumé : The behavioural symptoms in a 10-year-old boy with Lesch-Nyhan syndrome were effectively ameliorated by the behavior therapy techniques of systematic desensitization and extinction. Therapy was undertaken in a highly controlled environment. The hypothesis that the self-destructive behaviours in this syndrome were voluntary and maintained through continuous reinforcement was confirmed. Characteristic biting and other maladaptive behaviours were extinguished. Over a period of time it was possible to remove all the physical restraints previously used to prevent the boy injuring himself. During treatment his anxiety, associated with phobic reaction to being unrestrained, was reduced by nitrous oxide. At 1 1/2 years follow-up the boy continues to be symptom-free. He attends a special class at school and is learning to walk with crutches. It is emphasied that a trained and experienced therapist and a controlled environment are essential for the success of this form of behaviour therapy, and the dangers inherent in this method of treatment are discussed. Permalink : https://www.cra-rhone-alpes.org/cid/opac_css/index.php?lvl=notice_display&id=480 [article] Behavior therapy for a child with Lesch-Nyhan syndrome [Texte imprimé et/ou numérique] / Marilyn BULL, Auteur ; Francesca LAVECCHIO, Auteur . - 1978 . - p.368-375. Langues : Anglais (eng) in Developmental Medicine & Child Neurology > 20-3 (June 1978) . - p.368-375 Index. décimale : PER Périodiques Résumé : The behavioural symptoms in a 10-year-old boy with Lesch-Nyhan syndrome were effectively ameliorated by the behavior therapy techniques of systematic desensitization and extinction. Therapy was undertaken in a highly controlled environment. The hypothesis that the self-destructive behaviours in this syndrome were voluntary and maintained through continuous reinforcement was confirmed. Characteristic biting and other maladaptive behaviours were extinguished. Over a period of time it was possible to remove all the physical restraints previously used to prevent the boy injuring himself. During treatment his anxiety, associated with phobic reaction to being unrestrained, was reduced by nitrous oxide. At 1 1/2 years follow-up the boy continues to be symptom-free. He attends a special class at school and is learning to walk with crutches. It is emphasied that a trained and experienced therapist and a controlled environment are essential for the success of this form of behaviour therapy, and the dangers inherent in this method of treatment are discussed. Permalink : https://www.cra-rhone-alpes.org/cid/opac_css/index.php?lvl=notice_display&id=480

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