Behavior therapy for a child with Lesch-Nyhan syndrome / Marilyn BULL in Developmental Medicine & Child Neurology, 20-3 (June 1978)

Public ISBD [article]  inDevelopmental Medicine & Child Neurology > 20-3 (June 1978) . - p.368-375 Titre : Behavior therapy for a child with Lesch-Nyhan syndrome Type de document : Texte imprimé et/ou numérique Auteurs : Marilyn BULL, Auteur ; Francesca LAVECCHIO, Auteur Année de publication : 1978 Article en page(s) : p.368-375 Langues : Anglais (eng) Index. décimale : PER Périodiques Résumé : The behavioural symptoms in a 10-year-old boy with Lesch-Nyhan syndrome were effectively ameliorated by the behavior therapy techniques of systematic desensitization and extinction. Therapy was undertaken in a highly controlled environment. The hypothesis that the self-destructive behaviours in this syndrome were voluntary and maintained through continuous reinforcement was confirmed. Characteristic biting and other maladaptive behaviours were extinguished. Over a period of time it was possible to remove all the physical restraints previously used to prevent the boy injuring himself. During treatment his anxiety, associated with phobic reaction to being unrestrained, was reduced by nitrous oxide. At 1 1/2 years follow-up the boy continues to be symptom-free. He attends a special class at school and is learning to walk with crutches. It is emphasied that a trained and experienced therapist and a controlled environment are essential for the success of this form of behaviour therapy, and the dangers inherent in this method of treatment are discussed. Permalink : https://www.cra-rhone-alpes.org/cid/opac_css/index.php?lvl=notice_display&id=480 [article] Behavior therapy for a child with Lesch-Nyhan syndrome [Texte imprimé et/ou numérique] / Marilyn BULL, Auteur ; Francesca LAVECCHIO, Auteur . - 1978 . - p.368-375. Langues : Anglais (eng) in Developmental Medicine & Child Neurology > 20-3 (June 1978) . - p.368-375 Index. décimale : PER Périodiques Résumé : The behavioural symptoms in a 10-year-old boy with Lesch-Nyhan syndrome were effectively ameliorated by the behavior therapy techniques of systematic desensitization and extinction. Therapy was undertaken in a highly controlled environment. The hypothesis that the self-destructive behaviours in this syndrome were voluntary and maintained through continuous reinforcement was confirmed. Characteristic biting and other maladaptive behaviours were extinguished. Over a period of time it was possible to remove all the physical restraints previously used to prevent the boy injuring himself. During treatment his anxiety, associated with phobic reaction to being unrestrained, was reduced by nitrous oxide. At 1 1/2 years follow-up the boy continues to be symptom-free. He attends a special class at school and is learning to walk with crutches. It is emphasied that a trained and experienced therapist and a controlled environment are essential for the success of this form of behaviour therapy, and the dangers inherent in this method of treatment are discussed. Permalink : https://www.cra-rhone-alpes.org/cid/opac_css/index.php?lvl=notice_display&id=480

Outcome of high-risk neonates with ventriculomegaly / Edward A. LIECHTY in Developmental Medicine & Child Neurology, 25-2 (April 1983)

Public ISBD [article]  inDevelopmental Medicine & Child Neurology > 25-2 (April 1983) . - p.162-168 Titre : Outcome of high-risk neonates with ventriculomegaly Type de document : Texte imprimé et/ou numérique Auteurs : Edward A. LIECHTY, Auteur ; Marilyn BULL, Auteur ; R. L. GILMOR, Auteur ; Carolyn Q. BRYSON, Auteur Année de publication : 1983 Article en page(s) : p.162-168 Langues : Anglais (eng) Index. décimale : PER Périodiques Résumé : The authors evaluated 89 infants who had had computed tomography of the head and who were followed-up for a minimum of one year. In a large proportion with moderate ventriculomegaly spontaneous stabilization or regression occurred, with normal developmental outcome in a high percentage of cases. However, there was a statistically significant trend toward lower developmental scores as ventricular size increased. Many infants with ventricular enlargement will not develop progressive hydrocephalus, but their cognitive and psychomotor development may be affected. Permalink : https://www.cra-rhone-alpes.org/cid/opac_css/index.php?lvl=notice_display&id=561 [article] Outcome of high-risk neonates with ventriculomegaly [Texte imprimé et/ou numérique] / Edward A. LIECHTY, Auteur ; Marilyn BULL, Auteur ; R. L. GILMOR, Auteur ; Carolyn Q. BRYSON, Auteur . - 1983 . - p.162-168. Langues : Anglais (eng) in Developmental Medicine & Child Neurology > 25-2 (April 1983) . - p.162-168 Index. décimale : PER Périodiques Résumé : The authors evaluated 89 infants who had had computed tomography of the head and who were followed-up for a minimum of one year. In a large proportion with moderate ventriculomegaly spontaneous stabilization or regression occurred, with normal developmental outcome in a high percentage of cases. However, there was a statistically significant trend toward lower developmental scores as ventricular size increased. Many infants with ventricular enlargement will not develop progressive hydrocephalus, but their cognitive and psychomotor development may be affected. Permalink : https://www.cra-rhone-alpes.org/cid/opac_css/index.php?lvl=notice_display&id=561

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